Arrhythmogenic right ventricular dysplasia/cardiomyopathy

Curr Cardiol Rep. 2005 Jan;7(1):70-5. doi: 10.1007/s11886-005-0014-6.

Abstract

Arrhythmogenic right ventricular dysplasia/cardiomyopathy is recognized as an important cause of death in young patients, particularly athletes. In the past 5 years, cardiac MRI techniques have evolved rapidly in an attempt to improve the noninvasive diagnosis of this disorder. Steady-state free precession sequences and more rapid fat saturation techniques have permitted a comprehensive and well-tolerated examination. The first formal testing of diagnostic accuracy among a broad range of readers has recently been completed. Despite these advances, limited spatial resolution and interobserver variability have prevented successful implementation of these methods. Future approaches may include high-field imaging at 3 Tesla, and viability imaging to improve diagnostic accuracy.

Publication types

  • Research Support, Non-U.S. Gov't
  • Review

MeSH terms

  • Arrhythmias, Cardiac / etiology
  • Arrhythmogenic Right Ventricular Dysplasia / diagnosis*
  • Arrhythmogenic Right Ventricular Dysplasia / etiology
  • Arrhythmogenic Right Ventricular Dysplasia / genetics
  • Arrhythmogenic Right Ventricular Dysplasia / physiopathology
  • Death, Sudden, Cardiac / etiology
  • Forecasting
  • Humans
  • Magnetic Resonance Imaging / methods
  • Magnetic Resonance Imaging / trends*