Telangiectasia macularis eruptiva perstans with an associated myeloproliferative disorder

Int J Dermatol. 2004 Dec;43(12):922-4. doi: 10.1111/j.1365-4632.2004.02249.x.

Abstract

Telangiectasia macularis eruptiva perstans (TMEP) is a cutaneous form of mastocytosis. It has been rarely associated with an underlying myeloproliferative disorder. We report the case of a patient, while receiving treatment for thrombocytosis, with both platelet production and function inhibitors presented with TMEP. TMEP is often refractory to therapy; however, our patient responded to treatment with PUVA.

Publication types

  • Case Reports

MeSH terms

  • Female
  • Humans
  • Leg Dermatoses / drug therapy
  • Leg Dermatoses / etiology*
  • Mastocytosis, Cutaneous / drug therapy
  • Mastocytosis, Cutaneous / etiology*
  • Middle Aged
  • PUVA Therapy
  • Polycythemia Vera / complications
  • Skin Diseases, Vascular / drug therapy
  • Skin Diseases, Vascular / etiology*
  • Telangiectasis / drug therapy
  • Telangiectasis / etiology*
  • Thrombocytosis / complications*