Molecular analysis of iron overload in beta2-microglobulin-deficient mice

Blood Cells Mol Dis. 2004 Sep-Oct;33(2):125-31. doi: 10.1016/j.bcmd.2004.05.003.

Abstract

Beta2-microglobulin knockout (beta2m-/-) mice represent an instructive model of spontaneous iron overload resembling genetic hemochromatosis. The mechanism of iron accumulation in this mouse model may be more complex than involving the MHC class I-like protein HFE. We report that beta2m-deficient mice, like Hfe-/- mice, lack the adaptive hepatic hepcidin mRNA increase to iron overload. The inverse correlation of hepatic iron levels and hepcidin mRNA expression in six beta2m-/- mice underlines the importance of hepcidin in regulating body iron stores. In contrast to Hfe-/- mice, beta2m-deficient mice display increased expression of the duodenal iron transporters DMT1 and ferroportin 1. This result implicates a broader role of beta2m in mammalian iron metabolism, suggesting that (an) additional beta2m-interacting protein(s) could be involved in controlling iron homeostasis, and highlighting the emerging connection of iron metabolism with the immune system.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Biological Transport
  • Blotting, Northern
  • Duodenum / metabolism
  • Hemochromatosis
  • Iron / metabolism
  • Iron Overload / genetics*
  • Liver / metabolism
  • Mice
  • Mice, Knockout
  • RNA, Messenger / genetics
  • beta 2-Microglobulin / deficiency*
  • beta 2-Microglobulin / genetics

Substances

  • RNA, Messenger
  • beta 2-Microglobulin
  • Iron