[Demyelinating neuropathy and Sjögren's syndrome: a diagnostic pitfall]

A M Guennoc; P Corcia; T Maisonobe; T Lefrancq; B de Toffol; A Autret

doi:10.1016/s0035-3787(04)71025-5

[Demyelinating neuropathy and Sjögren's syndrome: a diagnostic pitfall]

Rev Neurol (Paris). 2004 Jul;160(6-7):717-20. doi: 10.1016/s0035-3787(04)71025-5.

[Article in French]

Authors

A M Guennoc¹, P Corcia, T Maisonobe, T Lefrancq, B de Toffol, A Autret

Affiliation

¹ Service de Neurologie et de Neurophysiologie Clinique, CHU Bretonneau, Tours, France. guennoc@med.univ-tours.fr

PMID: 15247864
DOI: 10.1016/s0035-3787(04)71025-5

Abstract

Introduction: Neuropathies induced by Sjögren's syndrome (SS) are usually axonal. Nevertheless some demyelinating neuropathies have been described in patients with SS. To date, the relationship between demyelinating neuropathies and SS remains imprecise.

Case report: A 75 year-old man presented with a chronic history of sensory disturbances linked to demyelinating neuropathy. Electroneuromyography revealed a demyelinating neuropathy and complementary tests revealed both Sjögren's syndrome (SS) and HMSN IA.

Conclusion: We suggested that an inherited affection might be researched before considering that demyelinating neuropathy might be a form of peripheral nervous system involvement in SS.

Publication types

Case Reports
English Abstract

MeSH terms

Aged
Brain / pathology
Demyelinating Diseases / complications
Demyelinating Diseases / diagnosis*
Demyelinating Diseases / pathology
Diagnosis, Differential
Humans
Male
Peripheral Nervous System Diseases / diagnosis
Sjogren's Syndrome / complications
Sjogren's Syndrome / diagnosis*