Nevi flammei affecting two contralateral quadrants and nevus depigmentosus: a new type of phacomatosis pigmentovascularis?

Am J Med Genet A. 2003 Jun 1;119A(2):228-30. doi: 10.1002/ajmg.a.20128.

Abstract

Here, we report on a 64-year-old-woman with nevi flammei affecting two contralateral quadrants, venous insufficiency of the right leg, and asymmetry of the arms, in association with a linear nevus depigmentosus. This combination of vascular and pigmentary abnormalities may represent a novel type of phacomatosis pigmentovascularis caused by non-allelic twin-spotting.

Publication types

  • Case Reports

MeSH terms

  • Female
  • Humans
  • Leg / blood supply
  • Middle Aged
  • Neurocutaneous Syndromes / genetics
  • Neurocutaneous Syndromes / physiopathology*
  • Port-Wine Stain / genetics
  • Port-Wine Stain / physiopathology*