The APC-independent anticoagulant activity of protein S in plasma is decreased by elevated prothrombin levels due to the prothrombin G20210A mutation

Blood. 2003 Sep 1;102(5):1686-92. doi: 10.1182/blood-2003-02-0620. Epub 2003 May 1.

Abstract

Protein S exhibits anticoagulant activity independent of activated protein C (APC). An automated factor Xa-based one-stage clotting assay was developed that enables quantification of the APC-independent activity of protein S in plasma from the ratio of clotting times (protein S ratio [pSR]) determined in the absence and presence of neutralizing antibodies against protein S. The pSR was 1.62 +/- 0.16 (mean +/- SD) in a healthy population (n = 60), independent of plasma levels of factors V, VIII, IX, and X; protein C; and antithrombin, and not affected by the presence of factor V Leiden. The pSR strongly correlates with the plasma level of protein S and is modulated by the plasma prothrombin concentration. In a group of 16 heterozygous protein S-deficient patients, the observed mean pSR (1.31 +/- 0.09) was significantly lower than the mean pSR of the healthy population, as was the pSR of plasma from carriers of the prothrombin G20210A mutation (1.47 +/- 0.21; n = 46). We propose that the decreased APC-independent anticoagulant activity of protein S in plasma with elevated prothrombin levels may contribute to the thrombotic risk associated with the prothrombin G20210A mutation.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Antibodies
  • Anticoagulants / pharmacology
  • Blood Coagulation / drug effects
  • Blood Coagulation / physiology
  • Blood Coagulation Tests
  • Factor Xa / metabolism
  • Factor Xa / pharmacology
  • Female
  • Heparin / pharmacology
  • Heterozygote
  • Humans
  • Male
  • Phospholipids / pharmacology
  • Point Mutation
  • Protein C / metabolism
  • Protein S / genetics*
  • Protein S / immunology
  • Protein S / metabolism*
  • Prothrombin / genetics*
  • Prothrombin / metabolism*

Substances

  • Antibodies
  • Anticoagulants
  • Phospholipids
  • Protein C
  • Protein S
  • Prothrombin
  • Heparin
  • Factor Xa