No abstract available
MeSH terms
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1-Deoxynojirimycin / analogs & derivatives
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Animals
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Enzyme Stability / drug effects
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Fabry Disease / drug therapy*
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Fabry Disease / metabolism
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Galactose / chemistry
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Galactose / pharmacology
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Gaucher Disease / drug therapy*
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Gaucher Disease / metabolism
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Glycoside Hydrolases / antagonists & inhibitors
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Humans
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Imino Sugars
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Molecular Weight
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Piperidines / chemistry
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Piperidines / pharmacology
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Protein Conformation / drug effects*
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Protein Folding*
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alpha-Galactosidase / antagonists & inhibitors
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alpha-Galactosidase / genetics
Substances
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Imino Sugars
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Piperidines
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1-Deoxynojirimycin
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migalastat
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Glycoside Hydrolases
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alpha-Galactosidase
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Galactose