Hemichorea as an initial manifestation of moyamoya disease: reversible striatal hypoperfusion demonstrated on single photon emission computed tomography

Mov Disord. 2002 Nov;17(6):1380-3. doi: 10.1002/mds.10245.

Abstract

We describe a case with unilateral moyamoya disease that showed progressive hemichorea as an initial manifestation. Single photon emission computed tomography showed perfusion defect in the contralateral basal ganglia although magnetic resonance imaging was unremarkable. Hemichorea improved along with normalization of perfusion after bypass surgery, suggestive of striatal hypoperfusion as the cause of hemichorea.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Brain Ischemia / diagnostic imaging*
  • Brain Ischemia / surgery
  • Carotid Stenosis / diagnostic imaging
  • Carotid Stenosis / surgery
  • Cerebral Revascularization
  • Chorea / diagnostic imaging*
  • Chorea / surgery
  • Corpus Striatum / blood supply*
  • Corpus Striatum / diagnostic imaging
  • Dominance, Cerebral / physiology
  • Female
  • Follow-Up Studies
  • Humans
  • Magnetic Resonance Imaging
  • Moyamoya Disease / diagnostic imaging*
  • Moyamoya Disease / surgery
  • Tomography, Emission-Computed, Single-Photon*