Abstract
The recent description of a large cohort of patients with the diagnosis of systemic sclerosis sine scleroderma (ssSSc) provided significant progress in our understanding of this entity. The prognosis of patients with ssSSc is, however, very variable, from benign in most cases to rapidly disabling in others. By reporting three new cases and analyzing previously published data, we discuss possible subsets and variants of the disease form.
MeSH terms
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Adolescent
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Adult
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Aged
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Biopsy, Needle
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CREST Syndrome / diagnosis
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CREST Syndrome / physiopathology
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Connective Tissue Diseases / diagnosis
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Connective Tissue Diseases / physiopathology
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Diagnosis, Differential
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Disease Progression
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Drug Therapy, Combination
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Female
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Humans
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Prognosis
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Risk Assessment
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Scleroderma, Localized / diagnosis*
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Scleroderma, Localized / physiopathology
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Scleroderma, Systemic / diagnosis*
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Scleroderma, Systemic / physiopathology
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Severity of Illness Index