Abstract
Severe hyperkalaemia in patients with congenital adrenal hyperplasia in association with aggravating factors such as acidosis and hypocalcaemia can cause life-threatening ventricular arrhythmias. Treatment of the underlying cause may be the only modality required in such cases. We report a 20-day-old male presenting with ventricular tachycardia due to electrolyte abnormalities in salt-losing congenital adrenal hyperplasia. Sudden cardiac deaths reported earlier in such cases thus gain credence.
MeSH terms
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Adrenal Hyperplasia, Congenital / complications
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Adrenal Hyperplasia, Congenital / diagnosis*
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Adrenal Hyperplasia, Congenital / therapy
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Electrocardiography*
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Follow-Up Studies
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Humans
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India
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Infant, Newborn
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Male
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Risk Assessment
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Severity of Illness Index
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Tachycardia, Ventricular / complications
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Tachycardia, Ventricular / diagnosis*
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Tachycardia, Ventricular / therapy
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Water-Electrolyte Imbalance / complications
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Water-Electrolyte Imbalance / diagnosis*
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Water-Electrolyte Imbalance / therapy