Ventricular tachycardia in congenital adrenal hyperplasia

Anaesth Intensive Care. 2002 Jun;30(3):380-1. doi: 10.1177/0310057X0203000322.

Abstract

Severe hyperkalaemia in patients with congenital adrenal hyperplasia in association with aggravating factors such as acidosis and hypocalcaemia can cause life-threatening ventricular arrhythmias. Treatment of the underlying cause may be the only modality required in such cases. We report a 20-day-old male presenting with ventricular tachycardia due to electrolyte abnormalities in salt-losing congenital adrenal hyperplasia. Sudden cardiac deaths reported earlier in such cases thus gain credence.

Publication types

  • Case Reports

MeSH terms

  • Adrenal Hyperplasia, Congenital / complications
  • Adrenal Hyperplasia, Congenital / diagnosis*
  • Adrenal Hyperplasia, Congenital / therapy
  • Electrocardiography*
  • Follow-Up Studies
  • Humans
  • India
  • Infant, Newborn
  • Male
  • Risk Assessment
  • Severity of Illness Index
  • Tachycardia, Ventricular / complications
  • Tachycardia, Ventricular / diagnosis*
  • Tachycardia, Ventricular / therapy
  • Water-Electrolyte Imbalance / complications
  • Water-Electrolyte Imbalance / diagnosis*
  • Water-Electrolyte Imbalance / therapy