Solitary schwannomas arising from the olfatory groove are extremely rare. Only 15 other cases have been reported so far. A case of olfatory groove schwannoma in a 19-year-old man with seizures and without neurological deficits is described. CT scan and MRI showed a tumour in the left frontobasal region. Left frontal craniotomy and excision of the tumour revealed a tumour in the region of the olfatory groove attached to the cribiform plate. The pathology, origin, and clinical characteristics of olfatory groove schwannomas are reviewed.