Recurrent lower respiratory tract infections in a 14-year-old boy with tracheobronchomegaly (Mounier-Kuhn syndrome)

Pediatr Pulmonol. 2000 Jun;29(6):476-9. doi: 10.1002/(sici)1099-0496(200006)29:6<476::aid-ppul10>3.0.co;2-r.

Abstract

Tracheobronchomegaly (Mounier-Kuhn syndrome) is characterized by dilatation of the central airways, tracheobronchial outpouchings, and chronic tracheobronchitis. Most cases are diagnosed in adulthood. We report the clinical, radiographic, and bronchoscopic findings in a 14-year-old boy with tracheobronchomegaly, ptosis of the right eyelid, and redundant skin and mucosa of the upper lip, who presented with a 2-year history of recurrent lower respiratory tract infections. Pediatricians should be aware of the possibility that tracheobronchomegaly may cause clinical symptoms in childhood and adolescence. Pediatr Pulmonol. 2000; 29: 476-479.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Blepharoptosis
  • Humans
  • Lip / abnormalities
  • Male
  • Recurrence
  • Respiratory Tract Infections / etiology*
  • Respiratory Tract Infections / pathology
  • Tracheobronchomegaly / complications*
  • Tracheobronchomegaly / microbiology