The use of [9,10-3H]myristate, [9,10-3H]palmitate and [9,10-3H]oleate for the detection and diagnosis of medium and long-chain fatty acid oxidation disorders in intact cultured fibroblasts

Adv Exp Med Biol. 1999:466:321-5. doi: 10.1007/0-306-46818-2_37.
No abstract available

MeSH terms

  • Acyl-CoA Dehydrogenase, Long-Chain
  • Cells, Cultured
  • Fatty Acid Desaturases / deficiency*
  • Fibroblasts / metabolism
  • Humans
  • Lipid Metabolism, Inborn Errors / diagnosis*
  • Lipid Metabolism, Inborn Errors / metabolism
  • Myristic Acid / metabolism*
  • Oleic Acid / metabolism*
  • Palmitic Acid / metabolism*
  • Tritium

Substances

  • Myristic Acid
  • Tritium
  • Oleic Acid
  • Palmitic Acid
  • Fatty Acid Desaturases
  • Acyl-CoA Dehydrogenase, Long-Chain