The esthesioneuroblastoma is a rare type of tumor located in nasal cavity, malignant, that is able to take a very aggressive growth pattern, but it has treatment with cure expectations when it is discovered in its initial stages by surgery or intensive radiotherapy and/or chemotherapy in the more developed ones. Due to its low incidence and its clinic presentation as a benign process that makes the patient takes it as a non important process, the esthesioneuroblastoma, as others malignant diseases of the nasal cavity, is frequently diagnosed at developed stages as this case that we present here.