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Zoledronic Acid in a Mouse Model of Human Fibrous Dysplasia: Ineffectiveness on Tissue Pathology, Formation of "Giant Osteoclasts" and Pathogenetic Implications.
Calcif Tissue Int. 2020 Dec;107(6):603-610. doi: 10.1007/s00223-020-00752-w. Epub 2020 Sep 1.
Calcif Tissue Int. 2020.
PMID: 32875378
Free PMC article.
RANKL Inhibition in Fibrous Dysplasia of Bone: A Preclinical Study in a Mouse Model of the Human Disease.
Palmisano B, Spica E, Remoli C, Labella R, Di Filippo A, Donsante S, Bini F, Raimondo D, Marinozzi F, Boyde A, Robey P, Corsi A, Riminucci M.
Palmisano B, et al. Among authors: spica e.
J Bone Miner Res. 2019 Dec;34(12):2171-2182. doi: 10.1002/jbmr.3828. Epub 2019 Aug 21.
J Bone Miner Res. 2019.
PMID: 31295366
Free PMC article.
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Constitutive expression of Gsα(R201C) in mice produces a heritable, direct replica of human fibrous dysplasia bone pathology and demonstrates its natural history.
Saggio I, Remoli C, Spica E, Cersosimo S, Sacchetti B, Robey PG, Holmbeck K, Cumano A, Boyde A, Bianco P, Riminucci M.
Saggio I, et al. Among authors: spica e.
J Bone Miner Res. 2014 Nov;29(11):2357-68. doi: 10.1002/jbmr.2267.
J Bone Miner Res. 2014.
PMID: 24764158
Free PMC article.
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Nanostring technology on Fibrous Dysplasia bone biopsies. A pilot study suggesting different histology-related molecular profiles.
Persichetti A, Milanetti E, Palmisano B, di Filippo A, Spica E, Donsante S, Coletta I, Venti MDS, Ippolito E, Corsi A, Riminucci M, Raimondo D.
Persichetti A, et al. Among authors: spica e.
Bone Rep. 2021 Dec 9;16:101156. doi: 10.1016/j.bonr.2021.101156. eCollection 2022 Jun.
Bone Rep. 2021.
PMID: 34950753
Free PMC article.
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GsαR201C and estrogen reveal different subsets of bone marrow adiponectin expressing osteogenic cells.
Palmisano B, Labella R, Donsante S, Remoli C, Spica E, Coletta I, Farinacci G, Dello Spedale Venti M, Saggio I, Serafini M, Robey PG, Corsi A, Riminucci M.
Palmisano B, et al. Among authors: spica e.
Bone Res. 2022 Jul 19;10(1):50. doi: 10.1038/s41413-022-00220-1.
Bone Res. 2022.
PMID: 35853852
Free PMC article.
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Osteoblast-specific expression of the fibrous dysplasia (FD)-causing mutation Gsα(R201C) produces a high bone mass phenotype but does not reproduce FD in the mouse.
Remoli C, Michienzi S, Sacchetti B, Consiglio AD, Cersosimo S, Spica E, Robey PG, Holmbeck K, Cumano A, Boyde A, Davis G, Saggio I, Riminucci M, Bianco P.
Remoli C, et al. Among authors: spica e.
J Bone Miner Res. 2015 Jun;30(6):1030-43. doi: 10.1002/jbmr.2425.
J Bone Miner Res. 2015.
PMID: 25487351
Free PMC article.
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