Abstract
Kawasaki disease is an acute multisystemic vasculitis occurring predominantly in infants and young children and rarely in adolescents and adults. At elderly age, Kawasaki disease may remain unrecognized with a subsequent delay in appropriate therapy and an increased risk of coronary artery aneurysms. We report a case of intravenous immunoglobulin- and aspirin-resistant Kawasaki disease and severe cardiovascular damage in an adolescent boy. The article discusses major issues associated with the management of refractory Kawasaki disease.
MeSH terms
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Adolescent
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Anticoagulants / therapeutic use
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Aspirin / therapeutic use
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Coronary Aneurysm / diagnosis*
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Coronary Aneurysm / etiology
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Drug Resistance
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Humans
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Immunoglobulins, Intravenous / therapeutic use
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Male
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Mucocutaneous Lymph Node Syndrome / complications
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Mucocutaneous Lymph Node Syndrome / diagnosis*
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Mucocutaneous Lymph Node Syndrome / drug therapy
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Rare Diseases / complications
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Rare Diseases / diagnosis*
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Rare Diseases / drug therapy
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Treatment Outcome
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Warfarin / therapeutic use
Substances
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Anticoagulants
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Immunoglobulins, Intravenous
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Warfarin
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Aspirin