Congenital pulmonary airway malformation: A report of two cases

World J Clin Cases. 2015 May 16;3(5):470-3. doi: 10.12998/wjcc.v3.i5.470.

Abstract

Congenital pulmonary airway malformation (CPAM), previously known as congenital cystic adenomatoid malformation is a congenital disorder of the lung similar to bronchopulmonary sequestration. In CPAM, usually an entire lobe of lung is replaced by a non-working cystic piece of abnormal lung tissue. This abnormal tissue will never function as normal lung tissue. The underlying cause for CPAM is not known. It occurs in approximately 1 in every 30000 pregnancies. The association between CPAM and malignancy has been well documented. There is a small risk (0.7%) of malignant transformation within the cyst. So early diagnosis and surgical resection is important to prevent the grave complications. Herein, we are reporting two interesting cases of CPAM and one belonged to Type II and other belonged to Type III of Stocker's classification.

Keywords: Congenital pulmonary airway malformation-Type II; Congenital pulmonary airway malformation-Type III; Surgical resection.

Publication types

  • Case Reports