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Page 1
Slower Calcium Handling Balances Faster Cross-Bridge Cycling in Human MYBPC3 HCM.
Pioner JM, Vitale G, Steczina S, Langione M, Margara F, Santini L, Giardini F, Lazzeri E, Piroddi N, Scellini B, Palandri C, Schuldt M, Spinelli V, Girolami F, Mazzarotto F, van der Velden J, Cerbai E, Tesi C, Olivotto I, Bueno-Orovio A, Sacconi L, Coppini R, Ferrantini C, Regnier M, Poggesi C. Pioner JM, et al. Circ Res. 2023 Mar 3;132(5):628-644. doi: 10.1161/CIRCRESAHA.122.321956. Epub 2023 Feb 6. Circ Res. 2023. PMID: 36744470 Free PMC article.
Calcium handling maturation and adaptation to increased substrate stiffness in human iPSC-derived cardiomyocytes: The impact of full-length dystrophin deficiency.
Pioner JM, Santini L, Palandri C, Langione M, Grandinetti B, Querceto S, Martella D, Mazzantini C, Scellini B, Giammarino L, Lupi F, Mazzarotto F, Gowran A, Rovina D, Santoro R, Pompilio G, Tesi C, Parmeggiani C, Regnier M, Cerbai E, Mack DL, Poggesi C, Ferrantini C, Coppini R. Pioner JM, et al. Front Physiol. 2022 Nov 7;13:1030920. doi: 10.3389/fphys.2022.1030920. eCollection 2022. Front Physiol. 2022. PMID: 36419836 Free PMC article.
IPSC derived cardiac fibroblasts of DMD patients show compromised actin microfilaments, metabolic shift and pro-fibrotic phenotype.
Soussi S, Savchenko L, Rovina D, Iacovoni JS, Gottinger A, Vialettes M, Pioner JM, Farini A, Mallia S, Rabino M, Pompilio G, Parini A, Lairez O, Gowran A, Pizzinat N. Soussi S, et al. Among authors: pioner jm. Biol Direct. 2023 Jul 27;18(1):41. doi: 10.1186/s13062-023-00398-2. Biol Direct. 2023. PMID: 37501163 Free PMC article.
R4496C RyR2 mutation impairs atrial and ventricular contractility.
Ferrantini C, Coppini R, Scellini B, Ferrara C, Pioner JM, Mazzoni L, Priori S, Cerbai E, Tesi C, Poggesi C. Ferrantini C, et al. Among authors: pioner jm. J Gen Physiol. 2016 Jan;147(1):39-52. doi: 10.1085/jgp.201511450. Epub 2015 Dec 14. J Gen Physiol. 2016. PMID: 26666913 Free PMC article.
Paradoxical prolongation of QT interval during exercise in patients with hypertrophic cardiomyopathy: cellular mechanisms and implications for diastolic function.
Coppini R, Beltrami M, Doste R, Bueno-Orovio A, Ferrantini C, Vitale G, Pioner JM, Santini L, Argirò A, Berteotti M, Mori F, Marchionni N, Stefàno P, Cerbai E, Poggesi C, Olivotto I. Coppini R, et al. Among authors: pioner jm. Eur Heart J Open. 2022 May 10;2(3):oeac034. doi: 10.1093/ehjopen/oeac034. eCollection 2022 May. Eur Heart J Open. 2022. PMID: 35919344 Free PMC article.
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