Juvenile colloid milium (JCM) is a rare, chronic, benign but cosmetically disturbing degenerative dermatosis, characterized by the appearance of translucent papules on sun-exposed areas before puberty. The juvenile form of colloid milium is thought to be caused by an inherited susceptibility to ultraviolet (UV) light, transmitted in an either autosomal dominant or recessive manner, eventually leading to keratinocyte degeneration. The prevalence of JCM is unknown due to the scarcity of case reports. This paper describes the case of a 10 years old male patient diagnosed with JCM which, according to the information available so far, is the first such case reported in Romania.