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116 results

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Long-term amikacin liposome inhalation suspension in cystic fibrosis patients with chronic P. aeruginosa infection.
Bilton D, Fajac I, Pressler T, Clancy JP, Sands D, Minic P, Cipolli M, Galeva I, Solé A, Quittner AL, Jumadilova Z, Ciesielska M, Konstan MW; CLEAR-110 Study Group. Bilton D, et al. Among authors: fajac i. J Cyst Fibros. 2021 Nov;20(6):1010-1017. doi: 10.1016/j.jcf.2021.05.013. Epub 2021 Jun 16. J Cyst Fibros. 2021. PMID: 34144923 Free PMC article. Clinical Trial.
Diagnosis of cystic fibrosis in adults with diffuse bronchiectasis.
Hubert D, Fajac I, Bienvenu T, Desmazes-Dufeu N, Ellaffi M, Dall'ava-Santucci J, Dusser D. Hubert D, et al. Among authors: fajac i. J Cyst Fibros. 2004 Mar;3(1):15-22. doi: 10.1016/j.jcf.2003.12.004. J Cyst Fibros. 2004. PMID: 15463882 Free article.
ENaCbeta and gamma genes as modifier genes in cystic fibrosis.
Viel M, Leroy C, Hubert D, Fajac I, Bienvenu T. Viel M, et al. Among authors: fajac i. J Cyst Fibros. 2008 Jan;7(1):23-9. doi: 10.1016/j.jcf.2007.04.003. Epub 2007 Jun 7. J Cyst Fibros. 2008. PMID: 17560176 Free article.
Abnormal electrochemical skin conductance in cystic fibrosis.
Hubert D, Brunswick P, Calvet JH, Dusser D, Fajac I. Hubert D, et al. Among authors: fajac i. J Cyst Fibros. 2011 Jan;10(1):15-20. doi: 10.1016/j.jcf.2010.09.002. J Cyst Fibros. 2011. PMID: 20920895 Free article.
A CFTR potentiator in patients with cystic fibrosis and the G551D mutation.
Ramsey BW, Davies J, McElvaney NG, Tullis E, Bell SC, Dřevínek P, Griese M, McKone EF, Wainwright CE, Konstan MW, Moss R, Ratjen F, Sermet-Gaudelus I, Rowe SM, Dong Q, Rodriguez S, Yen K, Ordoñez C, Elborn JS; VX08-770-102 Study Group. Ramsey BW, et al. N Engl J Med. 2011 Nov 3;365(18):1663-72. doi: 10.1056/NEJMoa1105185. N Engl J Med. 2011. PMID: 22047557 Free PMC article. Clinical Trial.
Ataluren for the treatment of nonsense-mutation cystic fibrosis: a randomised, double-blind, placebo-controlled phase 3 trial.
Kerem E, Konstan MW, De Boeck K, Accurso FJ, Sermet-Gaudelus I, Wilschanski M, Elborn JS, Melotti P, Bronsveld I, Fajac I, Malfroot A, Rosenbluth DB, Walker PA, McColley SA, Knoop C, Quattrucci S, Rietschel E, Zeitlin PL, Barth J, Elfring GL, Welch EM, Branstrom A, Spiegel RJ, Peltz SW, Ajayi T, Rowe SM; Cystic Fibrosis Ataluren Study Group. Kerem E, et al. Among authors: fajac i. Lancet Respir Med. 2014 Jul;2(7):539-47. doi: 10.1016/S2213-2600(14)70100-6. Epub 2014 May 15. Lancet Respir Med. 2014. PMID: 24836205 Free PMC article. Clinical Trial.
No easy road to better cystic fibrosis care in Eastern Europe?
De Boeck K, Fajac I. De Boeck K, et al. Among authors: fajac i. J Cyst Fibros. 2018 Jul;17(4):423-424. doi: 10.1016/j.jcf.2018.05.007. Epub 2018 May 31. J Cyst Fibros. 2018. PMID: 29859834 Free article. No abstract available.
An automated computed tomography score for the cystic fibrosis lung.
Chassagnon G, Martin C, Burgel PR, Hubert D, Fajac I, Paragios N, Zacharaki EI, Legmann P, Coste J, Revel MP. Chassagnon G, et al. Among authors: fajac i. Eur Radiol. 2018 Dec;28(12):5111-5120. doi: 10.1007/s00330-018-5516-x. Epub 2018 Jun 4. Eur Radiol. 2018. PMID: 29869171
Amikacin liposome inhalation suspension for chronic Pseudomonas aeruginosa infection in cystic fibrosis.
Bilton D, Pressler T, Fajac I, Clancy JP, Sands D, Minic P, Cipolli M, Galeva I, Solé A, Quittner AL, Liu K, McGinnis JP 2nd, Eagle G, Gupta R, Konstan MW; CLEAR-108 Study Group. Bilton D, et al. Among authors: fajac i. J Cyst Fibros. 2020 Mar;19(2):284-291. doi: 10.1016/j.jcf.2019.08.001. Epub 2019 Aug 23. J Cyst Fibros. 2020. PMID: 31451351 Free PMC article. Clinical Trial.
116 results