Strauss AW - Search Results

1

The PPAR pan-agonist bezafibrate ameliorates cardiomyopathy in a mouse model of Barth syndrome.

Huang Y, Powers C, Moore V, Schafer C, Ren M, Phoon CK, James JF, Glukhov AV, Javadov S, Vaz FM, Jefferies JL, Strauss AW, Khuchua Z. Huang Y, et al. Among authors: strauss aw. Orphanet J Rare Dis. 2017 Mar 9;12(1):49. doi: 10.1186/s13023-017-0605-5. Orphanet J Rare Dis. 2017. PMID: 28279226 Free PMC article.

2

Cardiac and skeletal muscle defects in a mouse model of human Barth syndrome.

Acehan D, Vaz F, Houtkooper RH, James J, Moore V, Tokunaga C, Kulik W, Wansapura J, Toth MJ, Strauss A, Khuchua Z. Acehan D, et al. J Biol Chem. 2011 Jan 14;286(2):899-908. doi: 10.1074/jbc.M110.171439. Epub 2010 Nov 9. J Biol Chem. 2011. PMID: 21068380 Free PMC article.

3

Cardiac metabolic pathways affected in the mouse model of barth syndrome.

Huang Y, Powers C, Madala SK, Greis KD, Haffey WD, Towbin JA, Purevjav E, Javadov S, Strauss AW, Khuchua Z. Huang Y, et al. Among authors: strauss aw. PLoS One. 2015 Jun 1;10(6):e0128561. doi: 10.1371/journal.pone.0128561. eCollection 2015. PLoS One. 2015. PMID: 26030409 Free PMC article.

4

The Effects of PPAR Stimulation on Cardiac Metabolic Pathways in Barth Syndrome Mice.

Schafer C, Moore V, Dasgupta N, Javadov S, James JF, Glukhov AI, Strauss AW, Khuchua Z. Schafer C, et al. Among authors: strauss aw. Front Pharmacol. 2018 Apr 11;9:318. doi: 10.3389/fphar.2018.00318. eCollection 2018. Front Pharmacol. 2018. PMID: 29695963 Free PMC article.

5

Elucidating the Beneficial Role of PPAR Agonists in Cardiac Diseases.

Khuchua Z, Glukhov AI, Strauss AW, Javadov S. Khuchua Z, et al. Among authors: strauss aw. Int J Mol Sci. 2018 Nov 4;19(11):3464. doi: 10.3390/ijms19113464. Int J Mol Sci. 2018. PMID: 30400386 Free PMC article. Review.

6

Diminished Exercise Capacity and Mitochondrial bc1 Complex Deficiency in Tafazzin-Knockdown Mice.

Powers C, Huang Y, Strauss A, Khuchua Z. Powers C, et al. Front Physiol. 2013 Apr 17;4:74. doi: 10.3389/fphys.2013.00074. eCollection 2013. Front Physiol. 2013. PMID: 23616771 Free PMC article.

7

Cardiac-specific VLCAD deficiency induces dilated cardiomyopathy and cold intolerance.

Xiong D, He H, James J, Tokunaga C, Powers C, Huang Y, Osinska H, Towbin JA, Purevjav E, Balschi JA, Javadov S, McGowan FX Jr, Strauss AW, Khuchua Z. Xiong D, et al. Among authors: strauss aw. Am J Physiol Heart Circ Physiol. 2014 Feb;306(3):H326-38. doi: 10.1152/ajpheart.00931.2012. Epub 2013 Nov 27. Am J Physiol Heart Circ Physiol. 2014. PMID: 24285112 Free PMC article.

8

A zebrafish model of human Barth syndrome reveals the essential role of tafazzin in cardiac development and function.

Khuchua Z, Yue Z, Batts L, Strauss AW. Khuchua Z, et al. Among authors: strauss aw. Circ Res. 2006 Jul 21;99(2):201-8. doi: 10.1161/01.RES.0000233378.95325.ce. Epub 2006 Jun 22. Circ Res. 2006. PMID: 16794186

9

Molecular and phenotypic heterogeneity in mitochondrial trifunctional protein deficiency due to beta-subunit mutations.

Spiekerkoetter U, Sun B, Khuchua Z, Bennett MJ, Strauss AW. Spiekerkoetter U, et al. Among authors: strauss aw. Hum Mutat. 2003 Jun;21(6):598-607. doi: 10.1002/humu.10211. Hum Mutat. 2003. PMID: 12754706

10

Tissue carnitine homeostasis in very-long-chain acyl-CoA dehydrogenase-deficient mice.

Spiekerkoetter U, Tokunaga C, Wendel U, Mayatepek E, Ijlst L, Vaz FM, van Vlies N, Overmars H, Duran M, Wijburg FA, Wanders RJ, Strauss AW. Spiekerkoetter U, et al. Among authors: strauss aw. Pediatr Res. 2005 Jun;57(6):760-4. doi: 10.1203/01.PDR.0000157915.26049.47. Epub 2005 Mar 17. Pediatr Res. 2005. PMID: 15774826

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