Abstract
This article reviews the clinical features, histopathology, genetics, and differential diagnosis of incontinentia pigmenti. Emphasis is placed on appropriate management strategies for patients with incontinentia pigmenti.
MeSH terms
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Diagnosis, Differential
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Eye / pathology
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Female
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Genetic Linkage
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Humans
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Incontinentia Pigmenti* / diagnosis
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Incontinentia Pigmenti* / genetics
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Incontinentia Pigmenti* / pathology
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Incontinentia Pigmenti* / therapy
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Male
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Skin / pathology
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X Chromosome / genetics