A case of ureteral malacoplakia in a hemodialysis patient is reported. A 64-year-old woman suffering from macrohematuria, was diagnosed as having a right ureteral tumor by means of computerized tomography and antegrade pyelography. Right nephroureterectomy with bladder cuff resection was performed. Pathological examination indicated malacoplakia; multiple Michaelis-Gutmann bodies were found. The patient did well postoperatively and was discharged without further complications. This case appears to be the twenty-first report of ureteral malacoplakia in the world.