Immunosuppressive effects of organic acids accumulating in patients with maple syrup urine disease

J Inherit Metab Dis. 1995;18(2):165-8. doi: 10.1007/BF00711757.
No abstract available

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Caproates / metabolism
  • Cells, Cultured
  • Hemiterpenes
  • Humans
  • Keto Acids / metabolism*
  • Lymphocyte Activation / drug effects*
  • Maple Syrup Urine Disease / immunology*
  • Mitogens / pharmacology
  • Pentanoic Acids / metabolism
  • Phytohemagglutinins / pharmacology
  • Valerates / metabolism

Substances

  • Caproates
  • Hemiterpenes
  • Keto Acids
  • Mitogens
  • Pentanoic Acids
  • Phytohemagglutinins
  • Valerates
  • 2-hydroxyisovaleric acid
  • alpha-keto-beta-methylvaleric acid
  • alpha-ketoisovalerate
  • alpha-ketoisocaproic acid