Anesthesia experience in an adult Silver-Russell syndrome: a case report

Akinobu Hibino; Ayaka Hibino; Yoshinori Kamiya

doi:10.1186/s40981-024-00704-5

Anesthesia experience in an adult Silver-Russell syndrome: a case report

JA Clin Rep. 2024 Apr 3;10(1):20. doi: 10.1186/s40981-024-00704-5.

Authors

Akinobu Hibino¹, Ayaka Hibino², Yoshinori Kamiya³

Affiliations

¹ Department of Anesthesiology, Shibata Hospital Niigata Prefectural Hospital, 1-2-8 Honcho, Shibata City, Niigata 957-8588, Japan. ruroninn@hotmail.com.
² Department of Anesthesiology, Niigata University Medical and Dental Hospital, 1-754 Asahimachi-Dori, Chuo-Ku, Niigata City, Niigata 951-8510, Japan.
³ Department of Anesthesiology and Pain Medicine, Gifu University Graduate School of Medicine, 1-1 Yanagido, Gifu City, Gifu 501-1194, Japan.

Abstract

Background: There are no reports of anesthesia use in adult patients with Silver-Russell syndrome (SRS). Here, we report our experience with anesthesia in an adult patient with SRS complicated by chronic respiratory failure.

Case presentation: A 33-year-old woman was clinically diagnosed with SRS. She had severe chronic respiratory failure, complicated by superior mesenteric artery syndrome. Percutaneous gastrostomy was scheduled for nutritional management under epidural anesthesia; however, soon after esophagogastroduodenoscopy was started, she lost consciousness and spontaneous respiration. The patient was urgently intubated and converted to general anesthesia. The end-tidal carbon dioxide tension was > 90 mmHg at intubation.

Conclusions: Adult SRS patients with chronic respiratory failure have a risk of CO₂ narcosis. SRS also requires preparation for difficult airway management during the perioperative period.

Keywords: Carbon dioxide narcosis; Difficult airway management; Epidural anesthesia; Percutaneous endoscopic gastrostomy; Russell-Silver syndrome.