Hump on head: Rare case of bi-frontal fibrous dysplasia

Kunal Singla; Nishant Goyal; Pulkit Mittal; Zahed Ali Qamer; Jitender Chaturvedi; Arvind Kumar

doi:10.25259/SNI_201_2023

Hump on head: Rare case of bi-frontal fibrous dysplasia

Surg Neurol Int. 2024 Jan 5:15:1. doi: 10.25259/SNI_201_2023. eCollection 2024.

Authors

Kunal Singla¹, Nishant Goyal¹, Pulkit Mittal¹, Zahed Ali Qamer², Jitender Chaturvedi¹, Arvind Kumar³

Affiliations

¹ Department of Neurosurgery, All India Institute of Medical Sciences, Rishikesh, Uttarakhand, India.
² Department of Pathology, All India Institute of Medical Sciences, Rishikesh, Uttarakhand, India.
³ Department of Pathology and Laboratory Medicine, All India Institute of Medical Sciences, Rishikesh, Uttarakhand, India.

Abstract

Background: FD is relatively rare in the craniofacial region, accounting for only 20% of all cases. Currently, two general subtypes of FD are recognized: monostotic and polyostotic. The monostotic form is more frequent, accounting for 75% to 80% of fibrous dysplasia cases.

Case description: An 18-year-old male presented with the complaint of bony-hard swelling over the forehead for 8 years. Radiology showed an expansile osseous lesion involving frontal bones. The patient underwent bi-frontal craniectomy with gross total resection of tumour mass with titanium mesh cranioplasty. His postoperative period was uneventful and was discharged on the seventh postoperative day.

Conclusion: The cases of monostotic skull fibrous dysplasia should be treated by resection of the affected bone and cranioplasty. However, a more conservative re-contouring may be carried out in cases with multifocal involvement or when the excision is considered risky due to proximity to the major venous sinuses.

Keywords: Fibrous dysplasia; Frontal; Hump on the head; Parietal.

Publication types

Case Reports