Vesical Haemangioma in Klippel-Trenaunay-Weber Syndrome: A Clinical Case Report

Cureus. 2023 Dec 5;15(12):e49952. doi: 10.7759/cureus.49952. eCollection 2023 Dec.

Abstract

Klippel-Trenaunay-Weber (KTW) syndrome, a rare vascular disorder, often presents with cutaneous capillary malformations and soft tissue hypertrophy. However, urinary tract involvement in the form of vesical haemangiomas is a seldom-encountered clinical condition. We present a case of a 37-year-old male with KTW syndrome who exhibited recurrent gross haematuria, prompting clinical evaluation. Initial diagnostic assessments revealed erythematous changes in the bladder, consistent with haemangiomas. Despite an initial biopsy and diathermy, the patient's symptoms recurred, leading to a subsequent management strategy involving laser fulguration. This case underscores the significance of recognizing cutaneous haemangiomas as potential indicators of urinary tract involvement in KTW syndrome and highlights the challenges in managing vesical haemangiomas, where a multidisciplinary approach is essential for optimal care.

Keywords: klippel-trenaunay-weber syndrome; laser fulguration; multidisciplinary approach; urinary tract involvement; vesical haemangioma.

Publication types

  • Case Reports