Revisiting Rosai Dorfman disease: A rare histiocytic disorder with nodal and extranodal involvement

Smily Sharma; Poonam Sherwani; Venkata S Arunachalam; Rahul Dev

doi:10.4102/sajr.v27i1.2729

Revisiting Rosai Dorfman disease: A rare histiocytic disorder with nodal and extranodal involvement

SA J Radiol. 2023 Oct 30;27(1):2729. doi: 10.4102/sajr.v27i1.2729. eCollection 2023.

Authors

Smily Sharma¹, Poonam Sherwani², Venkata S Arunachalam³, Rahul Dev²

Affiliations

¹ Department of Diagnostic and Interventional Radiology, All India Institutes of Medical Sciences (AIIMS) Jodhpur, Jodhpur, India.
² Department of Radiodiagnosis, All India Institutes of Medical Sciences (AIIMS) Rishikesh, Rishikesh, India.
³ Department of Imaging Sciences and Interventional Radiology, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Thiruvananthapuram, India.

Abstract

Rosai Dorfman disease is a rare but benign and self-limiting disorder. A case of Rosai Dorfman disease in a 16-year-old female with classic radiological and pathological findings is presented. T2W hypointense signal of the soft tissue masses was a distinguishing MRI feature.

Contribution: Rosai Dorfman disease is often overlooked in the differentials of lymphadenopathy and soft tissue masses on account of its rarity. This case report comprehensively discusses the imaging approach to this rare disorder.

Keywords: Rosai Dorfman disease; emperipolesis; histiocytosis; massive lymphadenopathy; sinus histiocytosis.

Publication types

Case Reports