Atrial Septal Defect Associated With Right Bundle Branch Block Masking Brugada Syndrome

Cyrus Moïni; Djamila Rahim; Nabil Belfeki; Damien Poindron; Audrey Lefoulon; Thibaut Moulin; Mehran Monchi; Nicolas Lellouche

doi:10.1016/j.jaccas.2023.101816

Atrial Septal Defect Associated With Right Bundle Branch Block Masking Brugada Syndrome

JACC Case Rep. 2023 Mar 30:13:101816. doi: 10.1016/j.jaccas.2023.101816. eCollection 2023 May 3.

Authors

Cyrus Moïni^{1

2}, Djamila Rahim², Nabil Belfeki³, Damien Poindron⁴, Audrey Lefoulon^{1

4}, Thibaut Moulin⁵, Mehran Monchi⁶, Nicolas Lellouche⁵

Affiliations

¹ Groupe Hospitalier Sud Ile-de-France (GHSIF), Melun, France.
² Department of Cardiology, Antony Private Hospital, Antony, France.
³ Department of Internal Medicine, Groupe Hospitalier Sud Ile-de-France (GHSIF), Melun, France.
⁴ Department of Cardiology, Les Fontaines Clinic, Melun, France.
⁵ Department of Cardiology, Henri Mondor University Hospital, Créteil, France.
⁶ Department of Intensive Care Unit, Groupe Hospitalier Sud Ile-de-France (GHSIF), Melun, France.

Abstract

A type 1 Brugada electrocardiogram pattern may be masked by typical right bundle branch block aspect. We present 2 cases (male patients, aged 18 and 22 years) of associated ostium secundum atrial septal defect with a right bundle branch block aspect and symptomatic confirmed Brugada syndrome. Both patients underwent cardiac defibrillator implantation. (Level of Difficulty: Advanced.).

Keywords: Brugada syndrome; atrial septal defect; electrocardiogram; interatrial communication; right bundle branch block; sudden cardiac death.

Publication types

Case Reports