Modern treatment of a Klippel-Trenaunay syndrome patient with Palma procedure

Vascular. 2023 Mar 9:17085381231161852. doi: 10.1177/17085381231161852. Online ahead of print.

Abstract

Klippel-Trenaunay syndrome is a rare congenital anomaly that is associated with abnormalities in the deep venous system. Operative intervention is often used only when patients fail conservative management for chronic venous insufficiency. We present a case of a deep venous abnormality requiring a saphenous vein crossover Palma procedure, in combination with a left femoral arteriovenous PTFE fistula to manage a non-healing wound from chronic venous insufficiency in a 22-year-old man. This case highlights updates for modern treatment tips for technical and medical management decisions to avoid early graft thrombosis.

Keywords: Klippel–Trenaunay syndrome; Palma procedure; arteriovenous fistula; vascular surgery.