Isolated Ventricular Inversion: A Rare Complex Congenital Heart Disease With Neonatal Cyanosis

Arthur Gavotto; Marie Vincenti; Sophie Guillaumont

doi:10.1016/j.jaccas.2022.09.012

Isolated Ventricular Inversion: A Rare Complex Congenital Heart Disease With Neonatal Cyanosis

JACC Case Rep. 2022 Nov 3:8:101642. doi: 10.1016/j.jaccas.2022.09.012. eCollection 2023 Feb 15.

Authors

Arthur Gavotto^{1

2}, Marie Vincenti^{1

2}, Sophie Guillaumont¹

Affiliations

¹ Pediatric and Congenital Cardiology Department, M3C Regional Center, University Hospital, Montpellier, France.
² PhyMedExp, University of Montpellier, Centre National de la Recherche Scientifique, Institut National de la Santé et de la Recherche Médicale, Montpellier, France.

Abstract

A 1-day-old girl was referred for a cardiology consultation for a mean saturation at 80% without respiratory distress. Echocardiography showed an isolated ventricular inversion. This entity is extremely rare, with fewer than 20 cases reported. This case report describes the clinical evolution and the complex surgical management of this pathology. (Level of Difficulty: Advanced.).

Keywords: VSD, ventricular septal defect; atrioventricular discordance; congenital heart disease; isolated ventricular inversion; pediatric.