Objective: To review the research progress of intraspinal solitary fibrous tumor (SFT).
Methods: The domestic and foreign researches on intraspinal SFT were extensively reviewed and analyzed from four aspects, including disease origin, pathological and radiological characteristics, diagnosis and differential diagnosis, and treatment and prognosis.
Results: SFT is an interstitial fibroblastic tumor with a low probability of occurrence in the central nervous system, especially in the spinal canal. In 2016, the World Health Organization (WHO) used the joint diagnostic term "SFT/hemangiopericytoma" according to the pathological characteristics of mesenchymal fibroblasts, which can be divided into three levels according to specific characteristics. The diagnosis process of intraspinal SFT is complex and tedious. It has relatively variable imaging manifestations and specific pathological changes of NAB2-STAT6 fusion gene, which often requires differential diagnosis with neurinoma, meningioma, etc. The treatment of SFT is mainly resection, which can be assisted by radiotherapy to improve the prognosis.
Conclusion: Intraspinal SFT is a rare disease. Surgery is still the main treatment. It is recommended to combine preoperative or postoperative radiotherapy. The efficacy of chemotherapy is still unclear. In the future, more studies are expected to establish a systematic diagnosis and treatment strategy for intraspinal SFT.
目的: 对椎管内孤立性纤维瘤（solitary fibrous tumor，SFT）的研究进展进行综述。.
方法: 广泛查阅国内外有关椎管内SFT的相关研究，从疾病来源、病理学及影像学特征、诊断及鉴别诊断、临床治疗方法及预后4 个方面进行总结及分析。.
结果: SFT是一种间质成纤维细胞源性肿瘤，中枢神经系统发生概率较低，椎管内更是罕见。2016年世界卫生组织（WHO）创造了联合诊断术语“SFT/血管外皮细胞瘤”来描述此类病变，并将其分为3级。椎管内SFT的诊断过程复杂且繁琐，其影像学表现相对多变，具有特异性的NAB2-STAT6融合基因病理学改变特征，常需要与神经鞘瘤、脊膜瘤等进行鉴别诊断。该病治疗以手术切除肿瘤为主，可辅助放疗以提升预后。.
结论: 椎管内SFT是一类罕见疾病，治疗仍以手术为主，建议联合术前或术后放疗，化疗疗效尚不明确。今后需要更多研究以针对椎管内SFT建立系统性诊疗策略。.
Keywords: Intraspinal solitary fibrous tumor; diagnosis; treatment.