SOD1-Related Cerebellar Ataxia and Motor Neuron Disease: Cp Variant as Functional Modifier?

Cerebellum. 2024 Feb;23(1):205-209. doi: 10.1007/s12311-023-01527-3. Epub 2023 Feb 9.

Abstract

We describe a novel superoxide dismutase (SOD1) mutation-associated clinical phenotype of cerebellar ataxia and motor neuron disease with a variant in the ceruloplasmin (Cp) gene, which may have possibly contributed to a multi-factorial phenotype, supported by genetic and protein structure analyses.

Keywords: Amyotrophic lateral sclerosis; Cerebellar ataxia; Ceruloplasmin; Neurodegeneration; SOD1.

Publication types

  • Case Reports

MeSH terms

  • Amyotrophic Lateral Sclerosis* / genetics
  • Cerebellar Ataxia* / genetics
  • Ceruloplasmin / genetics
  • Ceruloplasmin / metabolism
  • Humans
  • Motor Neuron Disease* / genetics
  • Mutation / genetics
  • Superoxide Dismutase / genetics
  • Superoxide Dismutase / metabolism
  • Superoxide Dismutase-1 / genetics
  • Superoxide Dismutase-1 / metabolism

Substances

  • Ceruloplasmin
  • SOD1 protein, human
  • Superoxide Dismutase
  • Superoxide Dismutase-1