•Primary myoepithelial carcinoma is rare with a handful of cases reported from the vulva.•There is no standard of treatment for primary myoepithelial carcinoma.•Current recommendations suggest excision with wide margins to be the best therapy.•Chemotherapy and immunotherapy should be considered in combination with excision.
Keywords: Myoepithelial; Primary Myoepithelial Carcinoma; Vulva; Vulvar Tumor; Vulvar cancer.
© 2022 The Authors. Published by Elsevier Inc.