Palisaded Neutrophilic and Granulomatous Dermatitis in a Patient With Churg-Strauss Syndrome: A Case Report and Literature Review

Cureus. 2022 Oct 8;14(10):e30085. doi: 10.7759/cureus.30085. eCollection 2022 Oct.

Abstract

Palisaded neutrophilic and granulomatous dermatitis (PNGD) is a rare reaction pattern that is frequently linked to several systemic diseases, including autoimmune disease, inflammatory bowel disease, and vasculitis. Churg-Strauss syndrome (CSS) is an uncommon systemic condition that occurs exclusively in patients with asthma or a history of atopy. It is characterized by extravascular necrotizing granuloma and hypereosinophilia. This case report describes an illustrative case of a 61-year-old Bahraini female who had been diagnosed with CSS and presented with PNGD. The PNGD appeared a few weeks after her oral corticosteroid medication was discontinued. The present case report aims to assist in accurately diagnosing PNGD, as rarely manifested in this case, thus aiding clinicians in improving patient care.

Keywords: asthma; churg-strauss syndrome (css); eosinophilic granulomatosis with polyangiitis (egpa); extravascular necrotizing granuloma and hypereosinophilia; palisaded neutrophilic and granulomatous dermatitis (pngd).

Publication types

  • Case Reports