Isolated congenital interruption of the right interlobar pulmonary artery with unilateral interstitial lung abnormality

Mitsukuni Sakabe; Kazunori Tobino; Kazuki Uchida; Yosuke Murakami; Yuri Hiramatsu; Hiroaki Ota; Takafumi Kawabata

doi:10.1016/j.rmcr.2022.101734

Isolated congenital interruption of the right interlobar pulmonary artery with unilateral interstitial lung abnormality

Respir Med Case Rep. 2022 Sep 6:39:101734. doi: 10.1016/j.rmcr.2022.101734. eCollection 2022.

Authors

Mitsukuni Sakabe¹, Kazunori Tobino^{1

2}, Kazuki Uchida¹, Yosuke Murakami¹, Yuri Hiramatsu¹, Hiroaki Ota¹, Takafumi Kawabata¹

Affiliations

¹ Department of Respiratory Medicine, Iizuka Hospital, 3-83 Yoshiomachi, Iizuka, Fukuoka, 820-0018, Japan.
² Department of Respiratory Medicine, Juntendo University, School of Medicine, 2-1-1 Bunkyo-Ku, Hongo, 113-8421, Japan.

Abstract

We report a case of an isolated congenital interruption of the right interlobar pulmonary artery with unilateral interstitial lung abnormality. 3D-CT with enhancement showed absent right interlobar pulmonary artery without any other abnormalities of the pulmonary artery and an enlarged inferior phrenic artery. High-resolution CT demonstrated ground-glass opacities, reticular changes, and small cysts in the right middle and lower lobes, which were compatible with interstitial lung abnormality. The patient was diagnosed with an isolated congenital interruption of the right interlobar pulmonary artery since chronic pulmonary thromboembolism, structural heart disease, systemic congenital disease, and systemic vasculitis were ruled out.

Keywords: Congenital interruption of right interlobar pulmonary artery CT; ECG, Electrocardiography; Interstitial lung abnormality; PE, Pulmonary embolism; UIP, Usual interstitial pneumonia.

Publication types

Case Reports