Prenatal diagnosis of a coronary-to-pulmonary artery fistula in a fetus with pulmonary atresia and ventricular septal defect

BMJ Case Rep. 2022 Jun 22;15(6):e249271. doi: 10.1136/bcr-2022-249271.

Abstract

Pulmonary atresia and ventricular septal defect (PA/VSD) demonstrate a wide variety of pulmonary and coronary artery abnormalities; additionally, coronary-to-pulmonary artery fistula (CPAF) is a rare manifestation of PA/VSD and is seldom detected during pregnancy. In this report, we present a case of prenatal diagnosis of CPAF in PA/VSD and impactful images in a neonate, which were obtained using fetal echocardiography and postnatal electrocardiography-gated 320-row CT. Prenatal diagnosis of CPAF can facilitate the provision of better therapeutic strategies after birth.

Keywords: Congenital disorders; Neonatal and paediatric intensive care.

Publication types

  • Case Reports

MeSH terms

  • Coronary Artery Disease*
  • Female
  • Fetus
  • Fistula*
  • Heart Septal Defects, Ventricular* / diagnostic imaging
  • Humans
  • Infant, Newborn
  • Pregnancy
  • Prenatal Diagnosis
  • Pulmonary Artery / abnormalities
  • Pulmonary Artery / diagnostic imaging
  • Pulmonary Atresia* / diagnostic imaging