Total Colonic Aganglionosis in Hirschsprung disease

Richard J Wood; Aaron P Garrison

doi:10.1016/j.sempedsurg.2022.151165

Total Colonic Aganglionosis in Hirschsprung disease

Semin Pediatr Surg. 2022 Apr;31(2):151165. doi: 10.1016/j.sempedsurg.2022.151165. Epub 2022 Apr 20.

Authors

Richard J Wood¹, Aaron P Garrison²

Affiliations

¹ Department of Pediatric Colorectal and Pelvic Reconstructive Surgery, Nationwide Children's Hospital, Columbus, OH, USA. Electronic address: Richard.Wood@nationwidechildrens.org.
² Division of Pediatric General and Thoracic Surgery, Cincinnati Children's Hospital Medical Center, Cincinnati, OH, USA.

PMID: 35690465
DOI: 10.1016/j.sempedsurg.2022.151165

Abstract

Total Colonic Hirschsprung Disease (HD) can be challenging from a diagnostic and management standpoint and occurs in around 8% of cases of HD. Long term outcomes are difficult to compare due to variation in length of aganglionosis, chosen surgical techniques, and terminology utilized in the literature. In this review we highlight some of the management controversies and clinical challenges and emphasize future areas of suggested collaboration and research.

Keywords: Total Colonic Hirschsprung disease.

Publication types

Review

MeSH terms

Hirschsprung Disease* / diagnosis
Hirschsprung Disease* / surgery
Humans