[Cardiac sarcoidosis: Diagnosis, prognosis and therapeutics]

Rev Med Interne. 2022 Apr;43(4):212-224. doi: 10.1016/j.revmed.2021.08.018. Epub 2022 Mar 18.
[Article in French]

Abstract

Sarcoidosis is a systemic granulomatous disease characterized by pulmonary involvement in most patients and more rarely by extrapulmonary involvement such as ocular, skin, salivary, lymph nodes and joints damages. Neurological and cardiac involvements are uncommon but are associated with increased morbidity and mortality. Cardiac sarcoidosis affects 5 to 20% of patients depending on the studies and autopsy studies even report cardiac involvement in 25% of sarcoidosis patients. This review aims to summarise main data on the diagnostic value of the different imaging techniques in cardiac sarcoidosis and to also detail the management of these patients who require a multidisciplinary approach.

Keywords: Anti-TNFα; Immunosuppressants; Immunosuppresseurs; Prognosis; Pronostic; Sarcoidosis; Sarcoïdose cardiaque; TNFα inhibitors; Traitement; Treatment.

Publication types

  • Review

MeSH terms

  • Granuloma / complications
  • Humans
  • Lymph Nodes / pathology
  • Myocarditis* / complications
  • Prognosis
  • Sarcoidosis* / complications
  • Sarcoidosis* / diagnosis
  • Sarcoidosis* / therapy