Spontaneous Resolution of Congenital Dural Venous Sinus Ectasia Associated With Polymicrogyria-Case Report

Zuzanna Kozłowska; Paulina Komasińska; Barbara Steinborn; Kinga Toboła-Wróbel; Marek Pietryga; Marta Szymankiewicz-Breborowicz; Tomasz Szczapa; Monika Bekiesińska-Figatowska

doi:10.3389/fped.2022.822551

Spontaneous Resolution of Congenital Dural Venous Sinus Ectasia Associated With Polymicrogyria-Case Report

Front Pediatr. 2022 Feb 28:10:822551. doi: 10.3389/fped.2022.822551. eCollection 2022.

Authors

Zuzanna Kozłowska¹, Paulina Komasińska², Barbara Steinborn², Kinga Toboła-Wróbel³, Marek Pietryga³, Marta Szymankiewicz-Breborowicz¹, Tomasz Szczapa⁴, Monika Bekiesińska-Figatowska⁵

Affiliations

¹ Department of Neonatology, Neonatal Biophysical Monitoring and Cardiopulmonary Therapies Research Unit, Poznan University of Medical Sciences, Poznan, Poland.
² Department of Developmental Neurology, Poznan University of Medical Sciences, Poznan, Poland.
³ Department of Obstetrics and Women's Health, Poznan University of Medical Sciences, Poznan, Poland.
⁴ Department of Newborns' Infectious Diseases, Chair of Neonatology, Poznan University of Medical Sciences, Poznan, Poland.
⁵ Department of Diagnostic Imaging, Institute of Mother and Child, Warsaw, Poland.

Abstract

Dural venous sinus ectasia belongs to a rare group of venous sinus malformations of unknown origin and uncertain prognosis. We report the first patient with idiopathic congenital ectasia of the confluence of sinuses with thrombosis associated with bilateral polymicrogyria. It may highlight the causative relation between ischemia within the central nervous system due to torcular herophili ectasia with thrombosis in early pregnancy and the development of cortical malformations in neonates. We also highlight the role of MR neuroimaging in the diagnosis of these entities.

Keywords: central nervous system; cortical malformations; neonate; neuroimaging; torcular herophili.

Publication types

Case Reports