Purpose: Pineal anlage tumors (PAT) are extremely rare malignant tumors in the pediatric population considered to be a variant of pineoblastomas. These tumors are characterized by a combination of neuroectodermal and heterologous ectomesenchymal components. PAT can be clinically aggressive and has a propensity to cerebrospinal fluid (CSF) dissemination. So far, only 13 cases of these tumors have been reported in the literature.
Case article: In this article, we report the case of an anlage tumor in a 3-year-old girl with a rapidly aggressive course.
Keywords: Central nervous system tumors; Pineal tumors; Pineoblastoma; Primitive pineal tumor.
© 2022. The Author(s), under exclusive licence to Springer-Verlag GmbH Germany, part of Springer Nature.