Protein-losing enteropathy managed with percutaneous enlargement of a restrictive atrial septal defect

Abstract

Protein-losing enteropathy is one of the most feared complications of the Fontan circulation. The diagnosis of protein-losing enteropathy in this setting should prompt a thorough investigation for the presence of a treatable hemodynamic impairment. In this report, we describe a complete reversal of protein-losing enteropathy following percutaneous enlargement of a restrictive atrial septal defect in a patient with a fenestrated lateral tunnel Fontan and severe mitral stenosis.

Keywords: Atrial septum; Cardiac catheterization; Cateterismo cardíaco; Double outlet right ventricle; Dupla saída do ventrículo direito; Enteropatia por perda de proteínas; Estenose mitral; Fontan procedure; Mitral stenosis; Procedimento de Fontan; Protein-losing enteropathy; Septo auricular.