Ecthyma Gangrenosum in an Infant with Interleukin-1 Receptor-Associated Kinase 4 Deficiency

J Pediatr. 2021 Dec:239:241-242. doi: 10.1016/j.jpeds.2021.08.015. Epub 2021 Aug 13.
No abstract available

Keywords: cardiac arrest; necrotizing fasciitis; septic shock.

Publication types

  • Case Reports

MeSH terms

  • Ecthyma / diagnosis
  • Ecthyma / immunology*
  • Ecthyma / pathology
  • Fatal Outcome
  • Gangrene
  • Humans
  • Infant
  • Interleukin-1 Receptor-Associated Kinases
  • Male
  • Primary Immunodeficiency Diseases / complications
  • Primary Immunodeficiency Diseases / diagnosis*
  • Pseudomonas Infections / diagnosis
  • Pseudomonas Infections / immunology*
  • Pseudomonas Infections / pathology
  • Pseudomonas aeruginosa / isolation & purification*
  • Sepsis / diagnosis
  • Sepsis / immunology*
  • Sepsis / pathology
  • Skin / immunology
  • Skin / microbiology
  • Skin / pathology*

Substances

  • Interleukin-1 Receptor-Associated Kinases

Supplementary concepts

  • IRAK4 Deficiency