Norwood With Obstructed Total Anomalous Pulmonary Venous Connection and Tracheoesophageal Fistula Repair: Operating Room Delivery

Kyle W Riggs; Nina M Price; Alan O'Donnell; Haleh Heydarian; Beth A Rymeski; David L S Morales

doi:10.1016/j.jaccas.2020.03.031

Norwood With Obstructed Total Anomalous Pulmonary Venous Connection and Tracheoesophageal Fistula Repair: Operating Room Delivery

JACC Case Rep. 2020 May 20;2(5):732-733. doi: 10.1016/j.jaccas.2020.03.031. eCollection 2020 May.

Authors

Kyle W Riggs¹, Nina M Price¹, Alan O'Donnell¹, Haleh Heydarian¹, Beth A Rymeski¹, David L S Morales¹

Affiliation

¹ Cincinnati Children's Hospital Medical Center, Heart Institute, Cincinnati, Ohio.

Abstract

A baby boy with prenatally diagnosed hypoplastic left heart syndrome variant with obstructed veins was born in the operating room (OR) and underwent emergent Norwood operation and repair of obstructed infra-diaphragmatic total anomalous pulmonary venous connection. Post-operatively, esophageal atresia with tracheoesophageal fistula was identified and repaired on day of life 11. The patient is thriving at 22 months of age. (Level of Difficulty: Advanced.).

Keywords: PV, pulmonary venous/vein; TAPVC, total anomalous pulmonary venous connection; TEF, tracheoesophageal fistula; congenital heart defect; double outlet right ventricle; pediatric surgery; pulmonary circulation.