Intraabdominal lesser sac metastasis from Ewing's sarcoma: An exceptional localization

Malek Bouhani; Imen Sassi; Ines Zemni; Ghada Sahraoui; Amine Bouida; Maher Slimene; Khaled Rahal

doi:10.1177/2050313X211022426

Intraabdominal lesser sac metastasis from Ewing's sarcoma: An exceptional localization

SAGE Open Med Case Rep. 2021 Jun 4:9:2050313X211022426. doi: 10.1177/2050313X211022426. eCollection 2021.

Authors

Malek Bouhani^{1

2}, Imen Sassi^{1

2}, Ines Zemni^{1

2}, Ghada Sahraoui^{2

3}, Amine Bouida^{1

2}, Maher Slimene^{1

2}, Khaled Rahal^{1

2}

Affiliations

¹ Department of Oncologic Surgery, Salah Azaiz Institute, Tunis, Tunisia.
² DUniversité de Tunis El Manar, Faculté de Médecine de Tunis, Tunis, Tunisie.
³ DDepartment of anatomopathology, Salah Azaiz Institute, Tunis, Tunisia.

Abstract

Ewing's sarcoma/primitive neuroectodermal tumor is rare and aggressive with a poor prognosis. Intraabdominal metastases are an uncommon condition. Metastasis in the lesser sac is an exceptional occurrence. To the best of our knowledge, this location has not been described previously. We report a case of a 15-year-old patient treated for Ewing's sarcoma of the left arm 6 years back. She had developed a suspicious mass in the lesser sac 6 years following her primary tumor. The histopathologic exam revealed a tumor with "small round cells" that were positive for CD99, confirming the relapse of Ewing's sarcoma. The relapse was successfully managed with chemotherapy and surgery. Intraabdominal, extraintestinal masses in patients treated previously for Ewing's sarcoma should be considered as Ewing's sarcoma relapse in the differential diagnosis. We fully describe the management of this atypical relapse, with different components of clinical, radiological, and histological findings.

Keywords: Ewing’s sarcoma; lesser sac; metastasis.

Publication types

Case Reports