Congenital Constriction Band With Lymphedema in a Neonate: A 17-Year Follow-Up After Single Stage Excision and Z-Plasty

Cureus. 2021 May 14;13(5):e15026. doi: 10.7759/cureus.15026.

Abstract

Congenital constriction band syndrome is a rare condition that presents with constriction bands affecting different types of extremities. Timely surgical intervention for moderate and severe stages of this condition can be performed either in a single stage or multiple stages. We report the case of a neonate who presented with a congenital constriction band and had excision of the constriction band and z-plasty reconstruction. The surgery was done in a single stage. This case highlights the outcome and safety of this single-stage surgery with Z-plasty reconstruction. At 17 years of age, he has a functional lower limb and excels in archery.

Keywords: congenital anomalies of the lower extremity; congenital constriction band syndrome; long-term outcome; single stage reconstruction; z-plasty.

Publication types

  • Case Reports