Treating Syndromic Craniosynostosis with Monobloc Facial Bipartition and Internal Distractor Devices: Destigmatizing the Syndromic Face

Clin Plast Surg. 2021 Jul;48(3):521-529. doi: 10.1016/j.cps.2021.03.002. Epub 2021 May 11.

Abstract

Monobloc and facial bipartition combined with distraction osteogenesis (MFBDO) has gained popularity over the past several years as a treatment of syndromic craniosynostosis, in part because this surgical technique effectively removes many stigmatic clinical features associated with the syndromic face. The objective of this study is to detail the surgical planning used to achieve medialization of the orbits and describe the authors' experience using MFBDO to destigmatize the syndromic face. By using MFBDO, hypertelorism, vertical orbital dystopia, and downslanting of the palpebral fissure were surgically corrected in all patients, thereby destigmatizing the syndromic face.

Keywords: Apert syndrome; Craniofacial dysostosis; Crouzon syndrome; Facial bipartition; Monobloc advancement; Pfeiffer syndrome; Syndromic craniosynostosis.

Publication types

  • Review

MeSH terms

  • Acrocephalosyndactylia / surgery*
  • Adult
  • Child
  • Craniofacial Dysostosis / surgery*
  • Face / surgery
  • Female
  • Humans
  • Male
  • Orthognathic Surgical Procedures / methods*
  • Osteogenesis, Distraction / instrumentation
  • Osteogenesis, Distraction / methods*