Complication of Hirschsprung's disease immediately after pregnancy: A rare case report

Int J Surg Case Rep. 2021 Jun:83:105893. doi: 10.1016/j.ijscr.2021.105893. Epub 2021 Apr 15.

Abstract

Introduction and importance: Hirschprung's disease (HD) is a rare congenital colonic disorder that may develop in adult age, often determining a poor life quality with complications needing an emergency surgical setting. The disease rarely presents as an acute intestinal obstruction like SV, which represents an abdominal emergency issue.

Case presentation: A few days after discharge from gynecology unit because of her first childbirth, a young woman with HD developed colonic obstruction due to sigmoid volvulus, which was treated with Hartmann's procedure.

Clinical discussion: Some months later, the patient underwent a two-stage Duhamel's procedure to restore the digestive tract's continuity. Both hospital periods were free of critical events.

Conclusion: The woman regained a good quality of life: Duhamel's procedure revealed as a safe technique to use in HD adult.

Keywords: Colorectal surgery; Duhamel; Hirschprung; Pregnancy; Volvulus.