Recurrent Miller-Fisher syndrome overlapping Guillain-Barrè syndrome and Bickerstaff brainstem encephalitis: A case report

Clin Neurol Neurosurg. 2021 Jul:206:106691. doi: 10.1016/j.clineuro.2021.106691. Epub 2021 May 17.

Abstract

Miller-Fisher syndrome (MFS) together with Guillan-Barré syndrome (GBS) and Bickerstaff brainstem encephalitis (BBE) are considered to form a continuous clinical spectrum of the same disease, possibly affecting the peripheral and/or central nervous systems, with monophasic symptoms. The frequency of overlapping clinical signs and the risk of recurrence are independent and very low, but no cases of GQ1b-seropositive recurrent MFS overlapping with GBS and BBE have been described so far. Here, we describe for the first time an atypical case of recurrent GQ1b-seropositive MFS overlapping GBS and BBE, 12 years after a previous GQ1b-seronegative typical MFS episode. Our case expands the clinical spectrum of recurrent MFS, and it should prompt clinicians to investigate the presence of anti-ganglioside antibodies in recurrent MFS even when these were negative in the previous episode, especially in those presenting with overlapping spectrum symptoms and a critically ill picture during the second episode.

Keywords: Anti-ganglioside antibodies; Bickerstaff brainstem encephalitis; Guillain-Barrè syndrome; Overlapping syndrome; Recurrent Miller-Fisher syndrome.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Autoantibodies / immunology
  • Autoantigens / immunology
  • Brain Stem
  • Encephalitis* / immunology
  • Encephalitis* / physiopathology
  • Female
  • Gangliosides / immunology
  • Guillain-Barre Syndrome* / immunology
  • Guillain-Barre Syndrome* / physiopathology
  • Humans
  • Miller Fisher Syndrome* / immunology
  • Miller Fisher Syndrome* / physiopathology
  • Recurrence

Substances

  • Autoantibodies
  • Autoantigens
  • Gangliosides
  • GQ1b ganglioside