An unusual secondary extramammary Paget's disease of vulva

Alvish Noel; Ramesh M Bhat; Sujaya V Rao; Shannon Fernandes

doi:10.4103/ijstd.IJSTD_69_19

An unusual secondary extramammary Paget's disease of vulva

Indian J Sex Transm Dis AIDS. 2020 Jul-Dec;41(2):210-212. doi: 10.4103/ijstd.IJSTD_69_19. Epub 2020 Nov 11.

Authors

Alvish Noel¹, Ramesh M Bhat¹, Sujaya V Rao², Shannon Fernandes²

Affiliations

¹ Department of Dermatology and, Father Muller Medical College Hospital, Mangalore, Karnataka, India.
² Department of OBG, Father Muller Medical College Hospital, Mangalore, Karnataka, India.

Abstract

Extramammary Paget's disease (EMPD) of the vulva is a rare disease that occurs mainly in postmenopausal women. It can be primary or secondary. Prognosis of primary EMPD is good, but when secondary, we need to find the underlying malignancy as the prognosis depends on it. Very few cases of secondary EMPD of the vulva have been reported till now. We hereby report a case of a 65-year-old postmenopausal woman with EMPD secondary to invasive adenocarcinoma with neuroendocrine features in the dermis and she was treated surgically followed by radiotherapy.

Keywords: Extramammary Paget's disease; genital malignancy; vulval carcinoma.

Publication types

Case Reports